Epoprostenol

Epoprostenol is a prostacyclin analog used for rapid ↓ PVR in severe PAH.

Indications

Long-term treatment of pulmonary vasodilation for:

  • Rapid reduction in pulmonary arterial pressures
  • WHO functional class III/IV patients with:
    • Idiopathic PAH
    • Familial PAH
    • Scleroderma spectrum disease with associated PAH

Contraindications

Principles

Epoprostenol:

  • Has two major pharmacological actions:
    • Direct vasodilation of pulmonary and systemic vasculature
    • Inhibition of platelet aggregation
  • Has a short half-life (2-6 minutes), and requires administration via continual infusion

Practice

Intravenous administration:

  • Initiate at 2ng/kg/min
  • Up-titrate by 1-2ng/kg/min every 15 minutes until
    • No further response seen
    • Dose limiting side effects reached:
      • Hypotension
      • Nausea
      • Vomiting
      • Headache
    • 20-40ng/kg/min reached

Complications

Key Studies


References